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Non diagnosed PAPVC induce large reverse venovenous shunt after modified Fontan surgery: A case report of a rare anomaly and embolization therapy

Version 3 2024-06-19, 05:58
Version 2 2024-06-06, 10:03
Version 1 2021-10-15, 09:11
journal contribution
posted on 2024-06-19, 05:58 authored by ZA Sani, A Ghasemi, S Mohammadzadeh, Z Khajali, M Behjati, Roohallah Alizadehsani, Abbas KhosraviAbbas Khosravi, S Nahavandi, SM Shariful Islam
Fontan operation is a reliable palliative surgery for patients with single ventricle physiology. Still, the development of complication is common; one of these complications that need to interventional approach is veno-venous collaterals between systemic and pulmonary veins. A 16-yearoldgirl with a history of modified Fontan operation at 9 years ago was referred with progressive cyanosis and dyspnea on exertion. In contrast trans-thoracic echocardiography (TTE), no fenestration was seen in Fontan circulation. Cardiac magnetic resonance revealed partial anomalous pulmonary vein connection (PAPVC) from left upper pulmonary vein to vertical vein and then into the in nominate vein and SVC with the reverse flow from superior vena cava (SVC) to left upper pulmonary vein(LUPV). This anomalous vein became severe engorged and tortuous. Possibly, LUPV and the verticalvein was dilated gradually as a result of increased pressure in the Fontan circuit. Finally, she underwent successful coil embolization in the midpart of the vertical vein. The oxygen saturation increased from80% to 93%.

History

Journal

Journal of Cardiovascular and Thoracic Research

Volume

13

Pagination

364-366

Location

Iran

ISSN

2008-5117

eISSN

2008-6830

Language

English

Publication classification

C4 Letter or note

Issue

4

Publisher

TABRIZ UNIV MEDICAL SCIENCES & HEALTH SERVICES

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